Rendu-Osler-Weber syndrome

AKA Hereditary hemorrhagic telangiectasia

Rendu-osler-weber syndrome
  • Etiology: AD – Dilation of small blood vessels on skin, mucosa and viscera (lungs, brain, liver)
  • Clinical:
    • Nose bleeds
    • Lesions on lips, nose, finger, skin – especially in sun exposed areas

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