Sturge-Weber syndrome

AKA Encephalotrigeminal angiomatosis

Struge weber syndrome

NOTE: Not a genetic condition, mutation is somatic and occurs before birth.

Port wine stain on forehead, scalp or around eyes due to over abundance of capillaries near surface of skin.


  • Triad:
    • Facial port wine nevus
    • Leptomeningeal angiomatosis
    • Glaucoma
  • Contralateral hemiplegia
  • Gingival overgrowth
  • Multiple impactions
  • Seizure disorder, mental retardation