Etiology:

Genetic disorder – Premature fusion of certain skull bones (craniosynostosis) – skull does not grow normally – affects shape of head and face

Clinical:

1. Skeletal abnormalities:

• Syndactyly
• Acrocephaly
• Brachicephaly

2. Oral complications:

• High palatal vault
• Posterior palatal cleft and bifid uvule
• Multiple impactions and malocclusions

3. Ovoid skull + horizontal supra-orbital groove

4. Early closure of coronal & sagittal sutures

• Mid third face underdeveloped
• Patent alveolar & frontal sutures

Treatment:

Surgery